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KMID : 1144020120080020109
Journal of Korean Association for Disability and Oral Health
2012 Volume.8 No. 2 p.109 ~ p.112
DENTAL CARIES CONTROL IN A GIRL WITH RECESSIVE DYSTROPHIC EPIDERMOLYSIS BULLOSA UNDER THE GENERAL ANESTHESIA : A CASE REPORT
Cho Seong-Hyeon

Song Je-Seon
Lee Hyo-Seol
Choi Hyung-Jun
Choi Byung-Jai
Kim Seong-Oh
Lee Jae-Ho
Abstract
Epidermolysis bullosa (EB) is an inherited skin disease characterized by blister formation of the skin following just minor trauma or spontaneously. The main classification of EB is based on the localization of the blistering. In epidermolysis bullosa simplex, the blister formation is intraepidermal; in epidermolysis bullosa junctionalis the blister formation in the epidermal-dermal junction; in the dystrophic forms of EB blister formation is intradermal. Oral manifestations of recessive dystrophic EB are characterized by rampant caries, crowding, microstomia, ankyloglossia, vestibular obliteration. Dental therapy may be well provided to patient with recessive dystrophic EB by using general anesthesia especially in case of poor cooperation. A two years old girl with recessive dystrophic EB visited our clinic for rampant caries. She was hospitalized for severe anemia and fever, and we provided dental therapy under general anesthesia. Extraction of incisors and stainless steel crown restoration of primary molars were performed.
KEYWORD
Recessive dystrophic epidermolysis bullosa, Rampant caries, General anesthesia
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